Portal vein thrombosis in Fontan-associated liver disease

Kaulitz R, Sieverding L, Hofbeck M.Cardiol Young. 2020 May 14:1-3. doi: 10.1017/S1047951120000992. Online ahead of print.PMID: 32406357



A 25-year-old patient with signs of cirrhosis on ultrasound and CT presented with portal vein thrombosis on routine follow-up examinations; retrograde hepatic wedge angiography demonstrated only the right-sided portal vein branch. Development of a portosystemic collateral vessel to the left-sided renal vein prevented signs of hypersplenism. This unique complication of portal vein thrombosis should be considered during long-term surveillance.