Twiddler’s syndrome with occult lead insulation damage in a child with epicardial pacemaker leads

Kramer P, Berger F, Peters B.Cardiol Young. 2020 May 19:1-2. doi: 10.1017/S1047951120001031. Online ahead of print.PMID: 32425140



We present a rare case of incidentally diagnosed Twiddler’s syndrome in a child 7 years after implantation of a dual-chamber pacemaker system with epicardial leads. During revision, an insulation defect of the ventricular lead was evident, despite unremarkable prior pacemaker lead testing. The lead was repaired and a new generator was suture-fixated to prevent re-occurrence of generator manipulation.