A rare childhood case of Behcet’s disease and chronic thromboembolic pulmonary hypertension


Wang AS, Rosenzweig EB, Takeda K.J Card Surg. 2020 May 17. doi: 10.1111/jocs.14610. Online ahead of print.PMID: 32419255



Background: Pulmonary embolism and chronic thromboembolic pulmonary hypertension (CTEPH) are rare complications of Behcet’s disease, especially in pediatric patients.

Aims/methods/results/conclusions: This case report highlights a presentation of CTEPH in an adolescent with Behcet’s disease. A multidisciplinary approach was required for managing this patient’s CTEPH, which successfully reversed the patient’s pulmonary hypertension.