Staged Surgical Management of Anatomically Corrected Malposition of Great Arteries


Kari FA, Siddiqui S, Farooqi KM, DiLorenzo MP, Bacha EA.World J Pediatr Congenit Heart Surg. 2020 May;11(3):352-354. doi: 10.1177/2150135119894491.PMID: 32294023



A nine-month-old girl diagnosed with anatomically corrected malposition (atrioventricular discordance, ventriculoarterial concordance, and malposed great arteries) complicated by multiple ventricular septal defects (VSD) and multifactorial left ventricular outflow tract obstruction (LVOTO) presented for management after pulmonary artery banding. She underwent interim palliation in the form of bilateral cavopulmonary connections, a modified Damus-Kaye-Stansel-type anastomosis, and subsequent staged one-and-a-half ventricle repair (1.5 repair) at the age of three years in the form of VSD closure, hemi-Mustard, and LVOTO resection.